ThanziMatenda ndi zokwaniritsa

Kodi matenda Ollier. Ollier a matenda: matenda ndi mankhwala

Mwina mungaganize kuti anu miyendo yaing'ono mwana kapena manja kukula pang'onopang'ono? Mwina matenda Ollier. Ndi matenda amene pali kuvutika fupa chitukuko cha mafupa, ndicho, dysplasia ake. Mayina ena amene atchulidwa matenda - mafupa angapo chondromatosis, unilateral kapena chondromatosis mafupa diskhondroplaziya. mutu matenda yake yaikulu inali m'malo mwa Lyons dokotala Olier. Matendawa anatulukira ndipo anafotokoza pogwiritsa ntchito X-ray mu 1899.

Kodi matenda Ollier

matenda amenewa amanena kuvutika kwa mafupa Bony m'dziko la matenda ambiri, kuphatikizapo odziwika bwino ambiri Moms ana m'chiuno dysplasia.

Matendawa zambiri amasonyezera ana, chifukwa cha zimene poyamba ankaganiza kuti matenda a ana. Tsopano imatsimikizirika kuti kudwala akanakhoza kupanga kuwonekera koyamba kugulu lake akuluakulu (zizindikiro kumachitika ngakhale mu m'badwo osiyanasiyana zaka 20-40). Ndi kobadwa nako chosayenerera, koma iye anapeza Patapita - ana aang'ono kapena unyamata - kutanthauza nthawi ya kukula kwambiri, pamene amakhala mapindikidwe akuoneka mafupa ndi / kapena nthenda chitukuko cha manja ndi miyendo.

matenda Ollier mu metaphyses wa yaitali mafupa tubular wa miyendo kuoneka zophuka wa chichereŵechereŵe. Disease akufotokozera makamaka fupa, chichereŵechereŵe, ndi zimfundo ndi manja ndi mapazi, makamaka mapazi ndi manja, komanso mu mafupa a chiuno, koma chimapezeka mu nthiti, sternum ndipo mutu.

Zophuka kapena enhondromy kupanga wosanjikiza lakunja la fupa woonda ndi Chimaona. Ndipotu, ndi mtima wabwino chotupa kuti akhoza kukhala mu zilonda (mwachitsanzo, chondrosarcoma). Mwamwayi, izi zimachitika kawirikawiri.

Panthawi yakutha msinkhu zophuka ziziyenda ndipo m'malo mwa fupa.

Choncho, Ollier matenda - wolemera cholowa matenda, calcification a mafupa cartilaginous imene likugwiritsidwanso ndi thickening metaphyses (mafupa yaitali khosi). Chifukwa pakuwonekera kwake akadali osadziwika. Nthawi zina, ndi autosomal lalikulu majini khalidwe.

Ofanana diskhondroplaziey matenda n'zochepa syndromes maffucci ndi Proteus. Poyamba, popanda chosaopsa zophuka chichereŵechereŵe ndi deformities chigoba khungu anapanga hemangioma - mdima wofiira mawanga mawonekedwe osasamba, wopangidwa Mitsempha. Mu chachiwiri osauka zotupa chosaopsa m'madera osiyanasiyana a thupi.

Amene anakhudzidwa ndi matenda

Poyamba ankaganiza kuti mafupawo chondromatosis osowa. Koma tsopano, pamene X-ray Kupenda ikuchitika ambiri zokwanira, kunapezeka kuti si m'chipani. Ngati zaka 20 zapitazo, limafotokonzera milandu 30 kuti tsopano kuwilikiza kaŵili.

Kudziwa isanayambike enieni zambiri n'zosatheka ngati kubadwa sipanatenge nthawi zonse kuphunzira ntchito X-ray zazikulu, makamaka oyambirira ubwana ndi chitukuko yoopsa, pamene zoona, pali Ollier matenda. Matendawa, ndi njira, atsikana chowululidwa pafupifupi kawiri zambiri kuposa anyamata.

zizindikiro

Kuti muphonye zizindikiro za matenda, makolo ayenera kukhala osamala ngati mwana:

  • yaitali chitukuko cha madera ena a nthambi / m'makona;
  • Amowabu asymmetry ndi zowononga mwa iwo;
  • ananena kupunduka;
  • pali misalignment a mafupa a chiuno ndi;
  • pano kupindika zimfundo wa valgus kapena mtundu varus.

Mfundo zonsezi n'zotheka kuganiza kuti mwana Ollier matenda.

Matendawa si nthawi yomweyo kuonekera pa kubadwa, koma pa zaka 1-4, muona kuti mwana msanga kuposa kuyembekezera, kuwonjezera mapazi kapena manja. Ichi ndi chizindikiro chachikulu cha matenda, chimene sitingakane. Onse a mwanayo bwinobwino, ngakhale kuti iye anapezeka ndi "matenda Ollier Mulungu."

Diskhondroplaziya nthawi zambiri zimakhudza nthambi imodzi Koma pali milandu la kugonjetsedwa onse. Ngati matendawa anakhudza pansi, mwanayo m'munsi kukula chifukwa kufupikitsa awo. Makamaka kwambiri kungokhala mafupa ngati ndondomeko pathological anayamba m'banda. Mapindikidwe chitani patsogolo yapang'onopang'ono. Kumene, kukhudzana ndi matenda, amakhala aafupi, thicker, kusintha gait, kupunduka zimawonedwa. Pakhoza kukhala varus kapena valgus chilema kwa bondo (zochepa kawirikawiri - pa proximal mapeto a femur kapena phazi), kupindika msana msana. Minofu ya manja pa matenda palibe.

kusintha Big imvera ndi phalanx, metatarsal ndipo zina, metacarpals. Iwo adzafupikitsidwa, anawonjezera, zosamveka ndiponso chichereŵechereŵe muli enlightenments ambiri.

matenda Ollier mwachionekere kwa fupa lothyoka chifukwa cha matenda iwo anayamba fupa cholakwika. Komabe, fractures zambiri seamlessly tchire.

Comorbidities

Diskhondroplaziyu akhoza ayende zotupa za ziwalo zina, ngakhale matenda okhudzana kukhala si nthawi zonse. Makamaka mu atsikana matenda Ollier a kumachitika teratoma wa n'kuwasanganiza ndi endocrine matenda, kuphatikizapo aakulu, kuphatikizapo kusamba m'banda ndi precocious msinkhu inapita ossification.

Komabe, chitukuko ndi zinayambanso kuyenda bwino ndi choti chotupa n'kuwasanganiza.

diagnostics

Kudziwa matenda Ollier, ndi woyamba kofunika kupanga roentgen. Palinso akhale fupa biopsy ndi chapamwamba kwambiri. Pa kudziwika matenda, odwala amafunika zonse cheke akuluakulu ndi dokotala, ngati n'koyenera mwamsanga kuti kusintha zilonda kuti chondrosarcoma.

matenda masiyanidwe

Masiyanidwe matenda a matenda Ollier Ndipotu, si kofunika pambuyo X-ray, chifukwa chithunzi ndi chondromatosis omveka bwino. Komabe, nkhani iliyonse ndi munthu, koma ya zizindikiro chowawa pafupifupi mobwerezabwereza, n'cholinga madokotala ayenera kulamulira angapo matenda ofanana.

Roentgen kumatha atypical Chondrodystrophy, hemihypertrophy kapena fupa manja, mapindikidwe rachitic ndi matenda ena. Komanso, chifukwa X-ray, Kwaletsedwa Recklinghausen matenda, zomwe kawirikawiri akhoza kusokonezedwa matenda Ollier. Mfundo yaikulu - kufunika kochita ndi x-ray mafupa lonse, osati gawo la izo.

Malangizo chithandizo

Diskhondroplaziya pa nthawiyo, mwatsoka, alibe njira zomveka mankhwala. Mosiyana Mwachitsanzo, matenda monga ntchafu dysplasia, chondromatosis ankachitira yekha ndi kukonzedwa opaleshoni ya mapindikidwe. Nthawi zina, izo zikusonyeza yokumba m'chiuno m'malo. Ena a chithandizo kuti wodwalayo alandire, - symptomatic ndi wothandiza.

Opaleshoni alowererepo akusonyeza makamaka kwa akulu, chifukwa malinga ndi kuyang'anila ano, pamene kukonzedwa opaleshoni pa zaka sukulu zotsatira zogwirizana Tinalandira, kutanthauza kuti mphamvu ya mankhwala opaleshoni aumbike lokha pa mapindikidwe, koma osati amphamvu. Komabe, mu kuvulala aakulu nkotheka opaleshoni ana, makamaka pankhani zala, amene kwambiri pamfundo pa matenda Ollier.

matenda amafuna kukhalabe olowa ndi fupa: odwala wasonyeza atavala nsapato mafupa ntchito braces mafupa ndi zipangizo zina akukonzekera mafupa. Odwala ayenera kuchita cholinga mwachindunji mankhwala kudwala ndiponso masewera olimbitsa thupi masewera zovuta.

Zothandiza monga olimbitsa ndi ntchito pa simulators wapadera. Izi zimathandiza kubwezeretsa minofu kamvekedwe ndi kulimbikitsa Mitsemphayi.

kaonedwe

Malinga ndi kafukufuku, nthawi zambiri mu msinkhu, chichereŵechereŵe m'malo mwa fupa (mwinamwake ndi chifukwa chake milandu wamkulu wa matenda wapezeka kwambiri kawirikawiri). Komabe, Mapa ndi zosakwana raduzhen ana: mapindikidwe, ngakhale pang'onopang'ono, koma pang'ono. Chimene oopsa Ollier matenda.

Matendawa kumaonekera kotero payekha pa nkhani iliyonse kuti madokotala ananena zawo akukhudzidwira ndi kovuta kuti aone unambiguously. Pamene zotupa angapo ndi yabwino koposa pa nkhani ya kusinthidwa umodzi m'madera ena. Single mapindikidwe akutitsogolera kuti kufupikitsa mmodzi wa miyendo choncho, ndi asymmetry awo, makamaka pankhani kwa ana aang'ono. Ndipo n'zosatheka kukonza. Komanso mu woyambirira wa khansa kumaonjezera ngozi ya deformities zosiyanasiyana za zala.

Transformation mu chondrosarcoma

Ngakhale kuti zilonda kusintha maganizo - chondrosarcoma - sizichitika kawirikawiri, komabe pali mwayi khansa. Makamaka izi zimachitika mu unyamata, ngakhale angapo kafukufuku panopa limasonyeza kuti zingachitike kwambiri mtsogolo. Pachifukwa ichi, odwala akulimbikitsidwa diskhondroplaziey zokambiranazo zonse ndi dokotala ndiponso mayeso zachipatala.

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