Thanzi, Matenda ndi zokwaniritsa
Hypertelorism - ndi chiyani ichi? Zimayambitsa ndi zizindikiro
Hypertelorism - mawu, imene inaperekedwa ndi kudwala yodziwika ndi kuwonjezeka kwambiri mu mtunda pakati pa ziwalo awiri wophatikizidwa. Nthawi zambiri anapezeka ocular hypertelorism, koma kusintha zina pathological kuchita panopa zachipatala. Izi ndi zimene ife kufotokoza kenako m'nkhani ino.
Hypertelorism - ndi chiyani ichi?
Mawu amenewa si chinthu chachilendo mu zolemba zachipatala. Hypertelorism -, monga tanenera kale, ndi kudwala amene anatsagana ndi kuwonjezeka mu mtunda pakati pa ziwalo awiri wophatikizidwa. Tikumbukenso kuti tanthauzo anayamba kugwiritsidwa ntchito osati kale - koyamba m'mabuku boma kuonekera mu 1924.
Mwachitsanzo, mankhwala odziwika monga kudwala ngati hypertelorism nsonga zamabele. Pankhaniyi, kuphwanya otchedwa unyinji Index - index, amene anatsimikiza ndi chiŵerengero pakati pa circumference wa pachifuwa pa mlingo wa nipple ndi mtunda wa pakati pawo. Kudwala si wodziimira ndi zambiri akufotokozera pa maziko a malformations kobadwa nako, monga Apert matenda, matenda Edwards.
Koma ambiri yozungulira hypertelorism - matenda amene pali ponso nthenda mu mtunda pakati mwake diso. Chotero boma ndi titadziwa - izo amawapeza mu masiku oyambirira pambuyo pa kubadwa.
ndi zimayambitsa matenda Kodi
Hypertelorism diso - kobadwa nako matenda, amene amaonera osiyana matenda chibadwa. Mwachitsanzo, kwambiri ambiri spaced mwake diso ali anaona ana ndi nefrofibromatozom, syndrome Apert, syndrome Down, mkate, Edwards ndi matenda ena amene anatsagana ndi malformations angapo a mwana wosabadwayo. Zifukwa zofanana ndi mwachindunji ndi monga kuvutika zosiyanasiyana kapangidwe ubongo kapena Chibade - ndi kukhalapo kwa zotupa, machiritso kwambiri mofulumira mbali Chigaza, zoopsa ubongo herniation ndi mphako.
Inde, n'zotheka kudziwa zinthu zina chiopsezo kuti akhoza kusokoneza yachibadwa chitukuko akalandire chithandizo , kapena hule zilipo kuvutika yoopsa chibadwa. Choncho, kungasokoneze chikhalidwe mwana unakhudza matenda anasamutsidwa ndi mayi woyembekezera, komanso kulowa mu thupi la poizoni, kuphatikizapo mankhwala katundu, mlingo waukulu wa mowa, mankhwala ndi zina zotero. D.
Hypertelorism: chithunzi ndi kugwirizana zizindikiro
Akuti hypertelorism ali digiri osiyana - odwala ena diso kwangochepetsako pang'ono chabe zawo, pamene ena ali amatangaza ndi dokotala anu kuzindikira chilema pambuyo tione choyamba pa mwanayo. ana awa ali ndi khalidwe kwambiri nkhope dongosolo la:
- Mtunda Pathologically lalikulu pakati pa nkhope lamkati la mmabowo mwake.
- Nthawi zambiri mapindikidwe palpebral fissures anawona - akhale ndi mawonekedwe osasamba, kapena kukhala asymmetrical mwapang'ono kwambiri.
- Palinso dongosolo khalidwe mphuno - nsana wake ndi lathyathyathya ndi lonse mphuno mlatho.
- Nthawi zambiri hypertelorism ana anapezeka ndi strabismus, zosiyanasiyana za kuwonongeka zithunzi, ndi mapindikidwe wa mitsempha chamawonedwe, vuto fungo.
Mwatsoka, pamwamba majini zizindikiro khalidwe osati kuphwanya dongosolo kutsogolo a Chigaza lapansi. Nthawi zambiri, ana ndi deformities phazi, nthenda chitukuko cha m'kamwa mwa, mkhutu kukula m'nzeru.
njira yodziwira
Kumene, mu nkhani iyi, ndikofunika matenda molondola, chifukwa muyenera kudziwa pamaso pa matenda makamaka chibadwa. Doctor linaŵerengera interorbit izi okruzhnostnoy-index, amene anatsimikiza ndi kugawa anayeza mutu circumference ndi mtunda pakati pa ngodya lamkati la maso slits, ndi nambala chifukwa ndi kuchulukitsa ndi 100. The kudwala ambiri ananena choncho kumene index kuposa 6.8 .
Komanso imachitika anamnesis makolo ndi kafukufuku chibadwa. Komanso, onetsetsani mwana wanu wadzikakamiza maginito kumveka kapena yopangidwa tomography mutu - njirayi angazindikire kuvutika fupa ndi kukhalapo kwa zotupa mu ubongo.
chithandizo matenda
Ngati ife kulankhula za hypertelorism, ndiye mankhwala enieni chofunika chokha kukachitika kuti pali chiwopsezo kwambiri ziwalo masomphenya ndi mitsempha mathero. Pankhaniyi bwino opaleshoni. Pa ndondomeko, dotolo amachita chigaza pulasitiki. Koma ndithudi, kusankha kugwira opareshoni kuyambira katswiri, ndi kusamala zifukwa zambiri, monga mmene mwana ndi kukhalapo kwa comorbidities. Opaleshoni nthawi anachita pamaso wodwala zaka ziwiri - ino ndi nthawi ntchito amapereka zotsatira mulingo woyenera.
Monga mankhwala zokhudza zonse, izo walangizidwa malangizo a matenda choyambirira. Kuyambira lero ndi zimadalira mankhwala kuchipatala.
Kupewa matenda ndi madokotala ananena zawo odwala
Hypertelorism - kani, izo ndi zokongoletsa chilema. Zoopsa monga syndromes ndi matenda amene anatsagana ndi matenda a. Choncho, chilemacho pakokha kuukira moyo wa mwanayo. The kuchotserapo okha milandu kumene zitsulo zokhazikapo mizati diso alibe amakhudza masomphenya wodwalayo.
Mokhudzana ndi kapewedwe, njira mwatsoka yeniyeni kuteteza ptologii anafotokoza kulibe. Kuchepetsa chiopsezo cha matenda intrauterine, pa mimba ayenera kuwunika thanzi, kudya bwino, kusiya kusuta, kumwa mowa, mankhwala ozunguza bongo zikanavulaza.
Pokonzekera mimba ndipo yayenera kutengedwa moyenera osati kusiya anakonza mogwirizana ndi zachibadwa a. Ena matenda majini akhoza matenda ngakhale utero. Kafukufuku majini pa mapulani mimba kudziwa mosavuta mwana wa kupatuka ndi.
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