Lennox-Gastaut syndrome (khunyu)

Lennox-Gastaut syndrome - mawonekedwe a khunyu (myoclonic-astatic). Chotero matenda chimake ikukhudza kuphatikiza zimandilimbikitsa ndi khunyu atonic, atypical pakalibe khunyu, anachedwa chitukuko maganizo makanda. Kwa nthawi yoyamba matendawa angasonyeze ana kwa wina ndi zisanu, makamaka kwa anyamata.

Matenda zambiri akufotokozera chifukwa kunditumiza ku ubwana matenda a ubongo, ndipo akuyamba ndi dontho mwadzidzidzi mwanayo. Patapita nthawi, pali zopweteka, khunyu, kusonyeza pang'onopang'ono chitukuko maganizo, ndi kuchepetsedwa nzeru.

Pang'onopang'ono, ndi kukula kwa mwana, chikhalidwe cha kukomoka zimasiyanasiyana. Kugwa m'malo mwa tsankho, achiwiri zowombetsa mkota, kuukira zovuta a khunyu.

Chifukwa cha zimene amaonetsa syndrome Lennox-Gastaut

Kumvetsa zimayambitsa matenda kuli kovuta zokwanira, koma kuti tsiku kudziwika ndi akuluakulu.

• The anomaly wa chitukuko ubongo.
• matenda akulu (kakhosi, encephalitis, chikuku).
• Majini matenda pathological ubongo (CNS, matenda kagayidwe kachakudya, tuberculous sclerosis).
• mwana anavulala pa ndime ya ngalande kubadwa (kubadwa asphyxia, kubadwa masiku asanakwane, etc.).
• CNS choipa mu nthawi perinatal, komanso asanakwane yobereka ndi asphyxia.

zizindikiro za PLGA

Lennox-Gastaut syndrome akhoza anazindikira ndi chizindikiro chofunika kwambiri - kwa khunyu. Ana amene anapezeka ndi "idiopathic khunyu" limanenanso za njira zosiyanasiyana za khunyu (zizindikiro) :

• paroxysms wa mathithi;
• atonic kukomoka;
• atypical kulibe;
• tsankho kukomoka;
• sternocleidomastoid omangana;
• myoclonic-astatic kukomoka;
• zimandilimbikitsa khunyu (zambiri kumachitika nthawi tulo);
• TC zowombetsa mkota khunyu.

Odwala ndi matenda a Lennox-Gastaut komanso ndi boma khalidwe la stupor ndi kusintha bwinobwino mu khunyu, retardation maganizo, chidziwitso ndi matenda umunthu.

Kupeza Vuto syndrome LH

Chikadzangotha zizindikiro woyamba wa matenda ayenera yomweyo kupempha thandizo la dokotala, itanani ambulansi. Childs, matenda a matenda ikuchitika ntchito ECG pakati kuukira.

LH Syndrome Chithandizo

syndrome Lennox-Gastaut amaliona ndi mankhwala ndi njira opaleshoni. Chithandizo ndi mankhwala udzabala zotsatira zabwino mu zosaposa 20% ya milandu. Mu opaleshoni njira mankhwala kuchotsa madontho mwadzidzidzi, ndi zothandiza kudula corpus callosum (callosotomy). Komanso, ntchito opareshoni walangizidwa mangolomera ya mitsempha vagus ndi kuchotsa zotupa mtima ndi malformations.

Komabe, tisaiwale kuti khunyu khalidwe la matenda izi zimavuta kuchitira; pamapeto iwo angayambitse wodwalayo zovuta kwambiri chikhalidwe ndi maganizo. Pafupifupi sachiranso zimandilimbikitsa khunyu, zimene zimachititsa kuti nzeru kuchepetsa.