Thanzi, Matenda ndi zokwaniritsa
Matenda Huntington a
matenda Huntington ndi osowa tinatengera matenda. Iwo anaulula kuti pafupifupi munthu mmodzi mwa zikwi khumi. matenda Huntington a amakwiya matenda pang'onopang'ono kwa wamanjenje dongosolo. Kulephera lalikulu ndi wapezeka awiri, inali kwambiri thunthu ubongo, masango maselo. Izi chipolopolo ndi caudate phata. Mbali zimenezi zimakhudzidwa lamulo zochita umasinthasintha pa mlingo chikumbumtima. Amachititsa matenda Huntington si ndendende bwino, koma asayansi kupitiriza kugwira ntchito pa nkhani imeneyi.
Zizindikiro za matenda zimachitika, kawirikawiri zaka zapakati pa zaka sate-faifi mpaka fifite. Mawonetseredwe zazikulu zimene zigwirizana pamodzi ndi matenda Huntington ndi awa:
- kayendedwe matenda;
- vutoli sakuyendetsa ntchito maganizo kwa maganizo.
Komanso, iwo kumachitika, ndi zizindikiro zina kugwirizana ndi matenda ya ubongo.
Ambiri odwala (90%) cha matenda Huntington a amakhala ndi magulu musanaganizire spasmodic (chorea). Izi nthawi zambiri chizindikiro choyamba.
kayendedwe matenda ena akatswiri monga chinthu chimodzimodzi, kapena kusintha minofu kamvekedwe, amavutika ndi kayendedwe zaufulu ndi mavuto postural momveka bwino za katchulidwe ka mawu (dysarthria), amavutika Pomeza (dysphagia), ndipo kuchepa magalimoto wachisokonezo chikhalidwe diso.
Progressive pang'onopang'ono kuchepa ntchito m'maganizo silipita matenda Huntington a, angayambe molumikizana ndi chitukuko matenda a m'maganizo. Odwala, makamaka, satha kuganizira, kutaya nthawi yaitali muzitha kukumbukira, luso kumvetsa ndi kupeza njira pakachitika mavuto. Kwa ena odwala, yodziwika ndi irritability, kusintha kugonana, kupsa mtima mphwayi, psychosis, maganizo.
Ngati pali zizindikiro za kudwala kwa matenda zolondola chofunika kutsimikizira kuli vuto pakati mbiri banja la abale. Ntchito kafukufuku katswiri ya ubongo mu onyamula jini nthenda zimathandiza kudziwa kusintha pang'ono liwiro, ulamuliro kayendedwe ndi zochita kale nthawi pamene matenda kukhala kulitchula.
Laboratory kusanthula magazi pogwiritsa ntchito zitsanzo DNA ntchito kupeza kuvutika mu magulu ena. Njirazi ndi monga:
- odwala - jini onyamula;
- odwala ndi umboni wa matenda;
- makanda m'mimba.
Komabe, tisaiwale kuti kafukufuku majini akhoza imfayo wamphamvu nkhawa zokwanira liyambe njira zina mimba.
Mu ndondomeko ya Kupeza Vuto chofunika ndi kuti achotse zinthu zina chitukuko matenda. Zikuphatikizapo, makamaka, akulandira zina m'gulu la mankhwala, sitiroko, nkhanza kwa nthawi yaitali mowa.
Today matenda si mankhwala. Komabe, ntchito miyeso achire umalimbana akuvutika zizindikiro, kuchepetsa mwamphamvu awo, komanso kusamalira maganizo odwala.
Mwa mankhwala akhoza kuchepetsa zovuta zizindikiro, phenothiazines ntchito. Iwo kulamulira chorea. Chithandizo amasankhidwa mokwanira mosamala, malinga ndi maonekedwe a mtima pofuna kupewa mavuto. Pitirizani ulamuliro wa chinthu chimodzimodzi minofu amatha mankhwala ena - dopamine agonists. Komabe, kuchita limasonyeza kuti chikhalidwe ichi, iwo sakhala ogwira kuposa matenda Parkinson.
Kuti kuchepetsa nkhawa, maganizo, irritability ndi zina psycho-maganizo matenda, odwala Kwalamulidwa physiotherapy.
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