Zizindikiro ndi mankhwala a matenda Landau-Kleffner

Landau-Kleffner matenda - ndi kuthi khunyu aphasia ana. Iwo amakhala kuphwanya ntchito mawu. Pankhaniyi, sindilola zigawo zikuluzikulu articulating wa kulankhula (phokoso kusinthidwa mwa mano, manenedwe, ndi pakhosi), ndi luso athandize phoneme mu chapakati mantha dongosolo mlingo. Mwa njira, ndi mu zina la kotekisi ubongo.

Matendawa amapezeka ana wathanzi kwathunthu. Choyamba kusiya luso atengere chilengedwe kunja, kenako sangakhale limaonetseratu momveka bwino komanso molondola zakukhosi kwawo. Mfundo yakuti mu ubongo wa mwanayo ndi kusintha pathological, zikusonyeza akugwirira. syndrome akutchulidwa mu 1957 asayansi awiri - Landau Kleffner. Choncho, maina awo ndi kuitana matenda.

The zimayambitsa matenda

Zimayambitsa matenda Landau-Kleffner si bwino kumatanthauza. Ngakhale nthawi zina, madokotala akhoza kudziwa chinthu zomwe zinachititsa kuti chitukuko cha matenda. Mu malo oyamba - ndi chatsekedwa mutu choipa, chotupa mu ubongo, matenda parasitic chifukwa mphutsi za nkhumba njoka zam'mimba za matepi - neurocysticercosis. chifukwa zingakhale ndi autoimmune demyelinating matenda, chimene chili ndi chiwonongeko cha nkhani woyera ya ubongo - myelin. Hule chitukuko cha matendawa komanso amatha kutupa mpanda chotengera m'chigawo cha ubongo. liwuli angapo a matenda n'zogwirizana ndi akusowa wa kwa mayitirokondiriyoni kupuma zovuta. Nthawi zina chifukwa kukhala kwambiri woonda kotekisi, chifukwa mwana osauka Chigawo anakhudzidwa.

Matendawa akhoza kukhala fulminant mawonekedwe. Kuti ndi dzulo zaka ziwiri kuyenda anayenda, analankhula, ndipo anali mwangwiro wathanzi mwana, ndipo tsopano n'kudzuka, sangathe uchimanga, ndi mawu ochepa. Nthawi zina matendawa pang'onopang'ono, crumb pang'onopang'ono wotaya umatha kulankhulana wapakamwa ndi kuzindikira mokwanira za zenizeni.

ndi zizindikiro ndi chiyani?

wamkazi wasayansi matenda anafotokoza Alexandrov N. Shii Landau-Kleffner syndrome, iye anati, palinso chifukwa cha otchedwa ubongo plasticity. Zinali ngati "restructured" bwino ntchito zake. Mu ndondomeko ya kusintha ndipo akufotokozera aphasia zosakhalitsa. Monga momwe zilili ndi anapeza mtundu, kuvulala ndi matenda oyamba ndi mtundu wa kudwala akhoza anapezeka ntchito akugwirira. Komanso, "choyamba belu" akhale khunyu khunyu, amene anaonekera pa mwana wa mbuzi. Iwo ali mu 70% milandu limodzi ndi isanayambike matenda.

Mozungulira kotala milandu onse, wodwalayo wotaya kulankhula ntchito kwa mwezi umodzi. Koma ambiri a imfa yake limapezeka pafupifupi yomweyo. Nthawi zina mwana sangathe kunena mau. Theka odwala aona matenda khalidwe. maganizo Sikuyenda lili. Ndi zaka, ndi khunyu kutha. Full kapena tsankho ayambe ntchito mawu zimachitika kwa zaka 16.

kuwonongeka wa kulankhula

Landau-Kleffner syndrome mwana umayamba ndi imfa ya ntchito ya kulankhula - ichi ndi chimodzi mwa zizindikiro zazikulu za matenda. Iwo amakhala ndi wapakamwa kapena Makutu agnosia - chakhungu kuzindikira, limene kusunga chikumbumtima ndipo tilinazo. Mbali yoyamba, wodwalayo sangathe kulankhula bwino. Lachiwiri - sangathe kuzindikira phokoso bwino ndi phokoso. Pankhaniyi, ndi mayankho wachibadwa matenda phonological audiogram.

The vuto lalikulu lagona ndendende m'munda wa tilinazo phokoso. Ngakhale izi, matendawa kumaonekera mu nthawi yobvuta pa chipangizo chinenero kupeza. Chakhungu kulankhula kubwezeretsa angakhale magulu a kwambiri. Aphasia amphamvu kwambiri odwala ena. Monga asayansi amati, milandu yovuta amapezeka odwala 6 mwa 77. Ngati mwana wakhala akuona kuyan'anila zazing'ono izo angapulumutse aphunzire kuwerenga ndi kulemba. Language chisokonezo akuwonetseredwa motere: mwanayo kukusokonezani makalata ndipo zikumveka cholakwika kumanga ziganizo, kodi sitinganenenso zakukhosi kwawo ndi zina zotero.

khunyu

Chipatala khunyu ndi anamuona pa 70-85% ya milandu anapeza syndrome Landau-Kleffner. Matenda mu wachitatu m'banja la ana amayamba limodzi khunyu kudwala. Izi - chiyambi cha matenda. chiwerengero cha odwala pakati kuukira ndi mawu matenda zingatenge zaka zingapo. Khunyu nthawi zambiri anakonza zaka zaka 4 mpaka 10. madokotala ambiri amanena kuti iwo alibe chidzachitika akadzakula. Ndiko kuti, pambuyo pa zaka 16 za khunyu sanalembedwepo.

Mu 58% odwala ndi kuliika khunyu tsankho. zimayambitsa awo kuwononga maselo a mu ubongo yofunika Chigawo chimodzi ubongo. Khunyu zimachitika 39% ya ana, khunyu ndi imfa ya chikumbumtima - pa 16%. Odwala ena poyera matenda myoclonic zokhudza nyama za pankhope ndi maapulo diso. 12% odwala khunyu imafalikira pa mlingo chibadwa.

matenda khalidwe

Iwo khalidwe pafupifupi onse odwala. 78% ya ana ndi mavuto khalidwe ngati anandipeza ndi matenda Landau-Kleffner. Akuluakulu sayenera kudabwa chifukwa chakuti mwana wawo kamodzi mtendere ndi chikondi mwadzidzidzi ankakwiya. Ukali - muyezo chizindikiro. Mkwiyo ukhoza kukula kwambiri ndipo amavutitsa, kuti mwana sangakwanitse kupirira popanda hospitalization bungwe amisala. Ena M'malo mwake, kudzipatula n'kukhala mwadzidzidzi. Amapewa kucheza ndi anthu akuvutika ndi nkhawa ndi maganizo obsessive.

Ana ena amaoneka ogontha kotheratu. Ena matenda cholakwika - satha kulankhula bwinobwino. Ndithudi, madokotala ndi zina zovuta kudziwa chimene chimayambitsa makhalidwe wachilendo kwa syndrome Landau-Kleffner. Ndipotu iye ndi khalidwe autistic yodziwika ndi zochitika monga sungathe kumanga zomveka kukwaniritsa pempholo, ndi obsessive kubwereza kwa mau omwewo, mawu. Ofooka ndende chidwi ndi kulalikira mwakhama anamuona pa 80% odwala. Ngakhale mavuto khalidwe ndi zizindikiro sekondale poyerekezera ndi mavuto kulankhula, ana ena akhoza kudabwa zachilendo, n'kosathandiza ndi chodabwitsa zosiyanasiyana. Mwachitsanzo, iwo akhoza maola kubwereza manja chomwecho.

mankhwala amakono

Poyamba chizindikiro cha matenda n'kofunika kuyamba chithandizo cha matenda Landau-Kleffner. Chipatala, amene mulankhula, adzatha kupereka njira zothetsera vutoli:

• Inde mankhwala;
• opaleshoni.

Zikatero, wodwalayo anatsegula chigaza ndi kuchotsa cholinga khunyu. Kuti tichite zimenezi, kudula ena a mafupa ndi chipolopolo yaikulu ya ubongo. Kenako, nkhani imvi a dokotala ndi wopanga ang'ambe thupilo. Adzapitiriza kuletsa mliri ndi kufala kwa nyemba epileptogenic. Ndiye Dura Mater ndi mafupa zimayikidwa mu malo. chilonda ndi sutured. Patapita masabata 6-7 pambuyo opaleshoni, mwana kuchipatala abwerera kunyumba kwawo. Pambuyo pa opaleshoni ana ndi Landau-Kleffner syndrome aona kusintha ntchito ozindikira ndipo maganizo.

Anti-kulanda

Chithandizo cha matenda Landau-Kleffner si nthawi zonse limayankha ntchito zosinthika. Nthawi zina amathandiza kuchotsa matenda mankhwala kuchipatala. Imakhala phwando anticonvulsants. Mwatsoka, iwo si nthawi zonse kupereka zabwino. Mwachitsanzo, "carbamazepine", "Phenobarbital", "Phenytoin" nthawi zambiri sizithandiza - aphasia zitha aziwonjezereka. Khunyu odwala zidzabwerezedwa ndi kubwezera munthu. Zimenezi ndi zoona makamaka kwa odwala ndi khunyu kawirikawiri kapena atypical pakalibe khunyu.

Komanso, madokotala nthawi zambiri ndi bwino "Nicardipine". Zimathandiza kuti asalalikire kashiamu ngalande. Zothandiza ndi utsogoleli wa mtsempha Popanga madzi a gamma globulin. ndipo ngati akhala mokwanira ogwira bongo "ethosuximide," "valproic asidi". Thandizo ndi benzodiazepines, makamaka "Clobazam" ndi "Midazolam". Koma iwo ayenera kuperekedwa kudzera m'mitsempha.

mankhwala ena

Landau-Kleffner syndrome, zizindikiro ndi mankhwala amene anafotokoza m'nkhani ino amapereka phwando "ntchito diazepam" asanagone. Izi mankhwala amapereka zotsatira zabwino. Therapy Kwalamulidwa kwa nthawi ya masabata 6 kupewa tachyphylaxis - kuchepetsa mofulumira kwenikweni ndi ntchito mobwerezabwereza kwa mankhwala. Kafukufuku wasonyeza kuti zikhonza kukhala zothandiza "levetiracetam". Amagwiritsidwanso bwino kuthandiza pa matenda a ubwana idiopathic khunyu focal, wakhunyu udindo magetsi tulo, yimitsira mafunde mosalekeza kukwera mu gawo lake pang'onopang'ono. Komanso bwino mankhwala a aphasia ndi khunyu, mankhwala "felbamate." Koma pamene inu mugwiritsa ntchito n'zotheka kukhala zosiyanasiyana mavuto, imene anthu amakonda anakumana aplastic magazi ndi chiwindi kukanika.

corticosteroids

Mankhwalawa Landau-Kleffner syndrome ndi thandizo corticosteroids. "ACTH" makamaka bwino kutsimikiziridwa. Amachepetsa mawonetseredwe a zizindikiro za anapeza khunyu aphasia, normalizes boma la akugwirira lapansi. Yaitali mankhwala ndi mankhwala tikulimbikitsidwa ambiri odwala. Komabe, dziŵani kuti si aliyense amene ali abwino m'thupi mankhwala njira.

Nthawi zambiri madokotala mankhwala mankhwala kwa odwala. Mwachitsanzo, "Prednisolone" chikuyendetsedwera m'nsinga pa miyezi itatu. mankhwala ntchito kwa chikhululukiro kupatsidwa ulemu. Nkofunika kukumbukira kuti kuchepetsa mlingo wa mankhwala amaganizira zisadzachitikenso zonse zizindikiro matenda. Kutalika okwana ndithudi ukhoza kuyambira miyezi sikisi zaka zingapo. Zodabwitsa ndizakuti, chithandizo corticosteroid ali kwambiri mavuto monga kunenepa kwambiri, matenda oopsa, shuga, ng'ala, kulephera impso, maganizo, amakhala wosangalala monyanyira syndrome ndi zina zotero. Komanso, iwo ali osavomerezeka kwa odwala amene ali ndi mavuto ndi chitetezo chokwanira, monga iwo anapitiriza nkhawa iye. Iwo contraindicated anthu ndi aseptic necrosis, TB kapena matenda amene maonekedwe chikwiyire ntchito yofunika roundworms.

Malingaliro a makolo

kusamalidwa ndi chidwi chofunika kwa mwana anapezeka ndi matenda Landau-Kleffner. Reviews a makolo akusonyeza kuti mwana ayenera kutenga makalasi kwa ndikuphunzitsidwa kulankhula, kulankhula pathologists. dokotala sangathe kubwezeretsa kulankhula ntchito. Koma magawo awa kuphunzitsa nyenyeswa kuti sanapirire, kubweretsa iye udindo, bungwe. Makolo amati ana kunja choncho mankhwala ndi anticonvulsant wabwino ndi antiepileptic mankhwala otchedwa "Keppra". Ifenso amalangiza "Depakine," koma limakhudza kungasokoneze kapamba, ena kusinthitsa mankhwala ofooketsa tizilombo. makolo ambiri akhala ananenanso kuti njira yabwino ndi matendawa - kukhwima mwana. Iye akukula - pang'ono ndi pang'ono kuwongolera mawu ake. Komanso, zaka kuthamanga oukira ndi paroxysms.

kaonedwe

Koma madokotala, iwonso kupitiriza kufufuza chomwe syndrome Landau-Kleffner. Photo odwala ndi nkhani video, mbiri yawo, anamaliza akatswiri yopapatiza mbiri - zonse ndi mbali ya kafukufuku. Madokotala anaona kuti mankhwala ntchito bwino kukachitika kuti mwanayo amapezeka misala, makalasi kulankhula. Full ayambe ntchito wapakamwa ndi mwachilungamo osowa. Kawirikawiri 2/3 la ana opulumutsidwa kapena zochepa kwambiri lachibadwa.