Harlequin Syndrome: Zizindikiro, mbali ndi mankhwala

makanda ndi omwe amakhala pachiopsezo kwambiri. Ngakhale m'mimba, iwo akhoza kukhudzidwa ndi zinthu zosiyanasiyana zoipa zimene chifukwa kudwala wa nyenyeswa. Chifukwa, anabadwa, kuyenda ali ndi mavuto ambiri. Mmodzi wa kupatuka koipa ndi Harlequin syndrome. Matendawa chikutchedwa khalidwe la Italy commedia dell'arte, amene anavala suti zopangidwa nyenyeswa zokongola nsalu.

Harlequin syndrome mu akhanda

Madokotala kupeza vuto yomweyo pambuyo pa kubadwa kwa mwana. Malinga ndi iwo, vuto Harlequin singalifotokoze angwiro dongosolo autonomic kuti salinso ufulu woteteza mtima kamvekedwe. Matendawa akhoza zidzayambike ndi yokoka yosavuta. Zachitikiranji zimenezi? Madokotala sangapereke Yankho mwamsanga. Osiyanasiyana zifukwa lonse: pa cholakwa yosavuta chitukuko yoopsa zosangalatsa moyo osauka, imbaenda mayi wapakati.

Matendawa angasonyeze monga lonse thupi, ndipo kokha m'madera ena a thupi. Ana awa, madokotala kunena, amakhala akudwala chimfine, chifukwa iwo kusokonezedwa thermoregulation. Kamwana nthawi iliyonse chaka adzakhala thukuta kwambiri, ndiye mwadzidzidzi kuti supercool, chifukwa cha matenda kulimbikira tizilombo Amawapatsa kwa iye. Komanso, syndrome amapereka kusapeza kulemera, kawirikawiri mwana akulira, izo wosakhazikika ndi kukwiya.

zizindikiro

Malinga ndi malipoti ena, matendawa akhoza kukhala zotsatira za asphyxia yoopsa kapena kuzipeza pa kubadwa intracranial choipa. Iye analinso matenda milandu ya zotupa za ubongo imene imalamulira kutentha ndi medulla oblongata. Mulimonsemo, malangizo yomweyo chifukwa katswiriyu. Azindikire matenda ndi losavuta: ndi chizindikiro chachikulu cha redness a khungu, pamene crumb atagona pa mbali yake. Pankhaniyi, malire a kusintha mtundu kumachitika chimodzimodzi mu mzere wa msana.

M'goli mbali mtundu wa thupi kumachitika maminiti angapo pambuyo kuwayika mwana. Zikuoneka matenda Harlequin. Photo ana ang'onoang'ono mainsaikulopediya zachipatala kusonyeza chithunzi yonyansa - kumtunda kwa thupi lawo ali ndi mtundu wabwinobwino, zilirimu amakhala ofiira owala, nthawi zina ndi kulocha bluish. Chodabwitsa ndi noticeable kwa mphindi zingapo. Akatswiri ena amanena kuti matendawa akhoza kukhala chizindikiro cha prematurity.

mawonetseredwe cutaneous

Ngati malongosoledwe a matenda ntchito zamankhwala, vuto Harlequin kumaonekera monga yaying'ono khungu keratinization. Si otchedwa granular wosanjikiza, m'malo kuonekera mipukutuyi inakhazikitsidwa m'zaka akulimbana a khungu. formations awa ndi mawonekedwe hexagonal, nthawi zambiri olekanitsidwa ndi ming'alu kwambiri wofiira. khungu pamene imvi kapena jaundiced.

Ana obadwa ndi matenda kawirikawiri ndi kuvutika ena: iwo angagwe mapindikidwe m'kamwa (milomo iye kukumbutsa nsomba), ectropion, yosayenera anayamba makutu kwambiri mosabisa. Nthawi zina, anapezeka ndi microcephaly, pamene mwana underdeveloped chigaza: chifukwa, iye anabadwa ndi ubongo waung'ono kwambiri. Ana otere kufa mu nthawi neonatal kapena pobadwa.

maonekedwe a matenda

Kids si nthawi zonse kufa, ngati iwo ali kudwala wa Harlequin. Matendawa si chiweruzo. matenda sangakhoze chitaperekedwa pambali, ngati msanga anapezeka ndi mwaluso, angathe kuchepetsa matenda nyenyeswa kukonzekera mwapadera. ana awa zisakuyenda osati kutentha, komanso bwino electrolyte. Chapped khungu utrudnyaet kupuma ndi kayendedwe. Mu ming'alu lalikulu atha kutenga kachilombo ndi kukhala sepsis.

Mwamwayi, matenda si sizachilendo. Pankhaniyi, khanda amayanjana kugonana zilibe kanthu kuti: kudwala atengeke anyamata ndi atsikana. Madokotala amanena kuti matendawa zambiri akuthamanga molimbika. Kuti madokotala ananena zawo nthawi zambiri zokwanira akumane. The aetiology wa matendawa akadali osadziwika.

mankhwala

Nyenyeswa Kwalamulidwa njira ya chithandizo, zomwe cholinga chake ndi kusunga yachibadwa kutentha thupi ndi olimba kosamala madzi electrolyte. Komanso ngati wodwala amafuna zakudya zachilendo, antiinflammatory, antibacterial mankhwala. Ntchito retinoids mu mawonekedwe a mafuta ndi makapisozi m'kamwa kwambiri kumawonjezera mlingo kupulumuka, ngati mwana wodwala matenda syndrome Harlequin. Chithandizo zimaphatikizapo kugwiritsa ntchito mankhwala, pamene mankhwala yogwira ndi isotretinoin ndi acitretin. Ngakhale izi, kupunduka kukhala pa khungu mpaka mapeto a masiku. Yacimwemwe odwala awa kwambiri yafupika.

Ngati matenda si chitaperekedwa n'zotheka kuchita popanda mankhwala. Makolo thandizo zokwanira mu nazale yachibadwa kutentha - mozungulira 20 madigiri. Zimaphunzitsa nyenyeswa monyanyira nyengo ayenera pang'onopang'ono: woyamba, ayenera atengere ozizira, ndiyeno yekha kuti kutenthetsa. Mukatero kuphunzitsa dongosolo autonomic ndi zotengera khoma mwana. Kumbukirani: ngati mwana anali thukuta, muyenera kusintha zovala yomweyo. njira zimenezi ayenera kupereka zotsatira zabwino.