Thanzi, Matenda ndi zokwaniritsa
Matenda Marfan akuti: zizindikiro zazikulu ndi zimayambitsa
Mtundu wina wa matenda aakulu matenda Marfan a. Kwenikweni ake tichipeza mu majini chintchito polumikiza zimakhala anthu, amene udindo kukhalabe khola dongosolo selo. Kukhomerera ziwiya mzake, ziwalo, minofu.
Mu syndrome Marfan amamvedwa ngati waphwanya zachilengedwe bwino chifukwa fibrilina masinthidwe, ndiko kuti, waukulu "nyumba" zinthu thupi. Kusintha chibadwa limathandiza kuti chitukuko cha pathologies ena a ziwalo, nthawi zambiri amavutika dongosolo mtima, ndi nkhani kusintha mu minofu fupa, kazinji kene mbagwa n'kudawa masomphenya.
Ndi zomvetsa chisoni kuvomereza, koma matenda Marfan panopa osachiritsika amatanthauza. Mwatsoka, asayansi sanapeze njira kuchotsa matenda moyo. Komabe, si anthu oipa, ndipo m'mbuyo Mulimonsemo sitingakhoze, chifukwa madokotala amatha kugwira mankhwala symptomatic. Izo ziri kale patsogolo tikaganizira mfundo yakuti zaka 20 zapitazo, anthu ndi matenda sakhala zaka zoposa makumi anayi. Tsopano odwala angayembekezere pafupifupi moyo wonse, kumene, malinga matenda anapangidwa nthawi, ndipo anayamba chithandizo pa siteji oyambirira a matenda.
Kufikira tsopano, mu Laboratories anayesedwa zosiyanasiyana mankhwala kulimbana ndi matendawa. Akukhulupirira kuti posachedwapa kukhala waukulu wothandizira wothandizila zochokera zoletsa. Ndiyeno, mwina, matenda Marfan si loopsa matenda kwa anthu ambiri, ndipo kenako kusamukira ku gulu la kusala pathologies mankhwala.
Kafukufuku genotype chosowa kwambiri. Monga ulamuliro, matenda Marfan ndi kunditumiza ku makolo ndi ana. Atalimbikitsidwa ndi chakuti mu mchitidwe dziko, n'kovuta kwambiri: kumodzi kwa anthu zikwi zisanu. Koma ngati makolo amadwala matenda izi, ndiye magawo fifite ayenera kuti tinatengera kwa mwanayo. % Only 25 pa ana si Marfan matenda kwa makolo awo, ndi chifukwa cha masinthidwe a umuna kapena dzira. Zizindikiro angasonyeze okha bwino kwambiri, ndipo kenako odwala ndi ofanana mbali, koma nthawizina chithunzi matenda ndi amaona kuti zizindikirozo kupanga kovuta kwambiri.
Marfan Syndrome: Zizindikiro
Mbali khalidwe la matenda imatengedwa kwambiri kutalika wodwalayo. mulibe choonadi nthawi zonse zimaonekera, malingana choncho payekha. Komanso kulabadira kukula ndi mawonekedwe a zala ndi zala, iwo unnaturally anatambasula, ndi yaitali ndi zopyapyala. Ngati ife kulankhula za odwala munthu kukula kwa thupi, ndi akanagwiritsa, monga manja ndi miyendo yaitali kwambiri poyerekezera ndi thupi. Monga tanena, odwala ambiri adzakhala ofanana nkhope. Zimenezi ndi zimenenso abnormally mkulu chigaza cholakwika malangizo kukula kwa mano, kwambiri akonzedwa maso. Komanso, odwala zambiri amalembedwa kupindika msana, mapazi mosabisa, chilema a chifuwa, matenda a mtima ndi mitsempha ya magazi.
Amenewa matenda ndi matenda Marfan a sizikutanthauza mapeto a moyo. Munthu sayenera kusiya pa chitukuko zina ndi kutsatila bedi zina monga wodwala kwambiri kudwala. Kumbukirani kuti matenda zingakhale, ndipo ngakhale kufunika kukhala ndi moyo wokangalika. Mwachitsanzo, pamodzi ndi onse kusewera masewera ophunzitsa, kuchita thupi, kuyenda pa mpweya wabwino, akasambire. Kumene, pangakhale mavuto osiyanasiyana, koma bwino olamulidwa ndi mankhwala.
Main kawirikawiri kwa kukaonana ndi dokotala, mwamsanga pamene angathe bwino ganizilani mkhalidwe wonse wa munthu ndi mwamsanga anatani kusintha kwake. Musataye, kulimbana ndi musati kutseka maso athu kuti mavuto alipo, ndipo udzachita bwino. Sangalalani tsiku lililonse, kotero kuti palibe mavuto sanathe zimalepheretsa inu kuchokera chachikulu m'moyo.
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