Thanzi, Matenda ndi zokwaniritsa
Rossolimo-Melkersson-Rosenthal syndrome: Zizindikiro, Chithandizo
syndrome Melkersson-Rosenthal Iwo amatchedwa matenda aakulu, ndi wa ku zizindikiro pachimake. The kudwala dzina la pali madokotala awiri maina. Melkersson anafotokoza zizindikiro ziwiri, ndi chachitatu amalembedwa Rosenthal. Chifukwa, matenda unatchedwa madokotala awiri.
Pa matenda Melkersson-Rosenthal
syndrome ndi polyetiological. Kwambiri kuti chitukuko lili zinthu zingapo:
- opatsirana ziwengo;
- matenda vasomotor ndi cholowa chimene chingawapangitse kukhala zidakwa kwa iwo;
- kudwala a dongosolo lymphatic m'dera la mutu ndi khosi;
- aakulu foci matenda odontogenic;
- sinusitis.
Pamaso pa syndrome Melkersson-Rosenthal n'zotheka neuro-osachiritsika zidakwa. Zisadzachitikenso matenda ndi nyengo. Makamaka syndrome Melkersson-Rosenthal amakhudza anthu pakati pa zaka 25 ndi 35 zakubadwa. Kodi zoyambitsa matenda hypothermia ndi uchidakwa, komanso chiwerengero cha mankhwala. kuphatikizidwa amgwirizano ali wamba - 75% milandu onse. kawirikawiri - kumbali.
Zizindikiro za matenda Melkersson-Rosenthal
Syndrome akuwonetseredwa kutupa kwa milomo ndi masaya. Kenako kufooketsa minofu nkhope. Munthu amakhala ovuta Ndikuchepetsa maso, kulankhula, ngodya m'kamwa anathira madzi. Mu 30 peresenti ya odwala kukhala maso youma kapena madzi. About 20% - kumatheka kuzindikira mawu kumlingo kuti amakhala wosasangalala. Kodi wina zimaonetsa Melkersson-Rosenthal syndrome zizindikiro? Pafupifupi 80% odwala kuwonjezera kutupa kwa milomo anawona reddening amphamvu ukuwonjezeka chinenero, pamwamba pake amakhala m'goli, vuto. Theka la odwala akukumana kwambiri mutu, khunyu masikono.
Kodi aliyense amakhala ndi kudwala ndi?
ndi zizindikiro za matenda oziziritsa yodziwika Rossolimo-Melkersson-Rosenthal chiyani? Poyamba, m'pofunika kutchula kuti Rossolimo - ndi dzina la dokotala lachitatu, amene 1901 anafotokoza makroheylit (matenda mkamwa, kuchuluka kukula) osakaniza nkhope mitsempha paresis. Kenako anapanga Melkersson. Koma popeza matenda kufotokoza Rossolimo dzina lake nthawi zina amagwiritsidwa ntchito mu kudwala kwa mutuwo.
Oziziritsa matenda kuwululidwa mwa cholinga zoona. Iwo akhoza chimaonetsera:
- mutu (migraine);
- nkhope asymmetry ;
- nkhope ziwalo minofu nkhope ;
- chizindikiro Bell lagophthalmos;
- xerophthalmia;
- hyperacusis;
- dysarthria;
- angioneurotic edema wa nkhope (zambiri milomo);
- fissured manenedwe ndi macroglossia;
- dizgevzii ndi ageusia;
- granulomatous cheilitis.
Monga tawerenga syndrome?
Melkersson-Rosenthal syndrome, amene ali zithunzi m'nkhani ino zingadziŵike ndi matenda. Pankhaniyi unachitika:
- serological mayesero;
- X-ray, ngati pali kukayikirana kuti matendawa zayamba chifukwa matenda (HIV, chindoko, Lyme matenda, sarcoidosis);
- electromyography;
- Maginito kumveka kulingalira ubongo;
- Kupenda Neuropathy.
Inde
Kodi matenda a Melkersson-Rosenthal? Matendawa amayamba ndi kutupa kwa khungu. Izo ndiye propagates kwa mucosa m'kamwa. Kuwonjezera kukula mlomo: pamwamba - kwambiri m'munsi - zochepa. Mukhoza kubva ya mitsempha nkhope, ndipo kenako kukhala ziwalo.
Matendawa ali ndi makhalidwe isanayambike pachimake. Kutupa akufotokozera maola angapo. Kawirikawiri yaikulu ndi kwathunthu likuthandiza milomo, amene utoto wofiira owala, nthawi zina bluish kulocha akuwonekera. Kuzungulira pakamwa akhoza kupanga ming'alu. Posasangalala kulankhula, zovuta ndi kudya.
Kodi matenda a Melkersson-Rosenthal aakulu? matendawa komanso akuyamba ndi kutupa. Koma ndi nthawi zonse, kumaonjezera okha kapena amachepetsa nthawi. Edema kusungidwa pa nkhope ndi M'mimbamo m'kamwa.
Ndi mtundu chosowa cha matenda Melkersson-Rosenthal, pamene kutupa masaya okha. Mwachibadwa, izi ziri mmodzi wa iwo. Pa lamkati masaya mbali bwino okhala mano. chikhalidwe ichi amatchulidwa ndi mawu akuti "granulomatous awiri." Palibe zizindikiro za kutupa.
chithandizo
Kodi Melkersson-Rosenthal syndrome? Madokotala amagwiritsa ntchito njira opaleshoni kapena ndiwofatsa. Poyamba, wodwala anafufuza kudziwa pathologies kuti zingachititse matenda. Opaleshoni chithandizo samaletsa zisadzachitikenso, ndipo ntchito kwambiri popanga zodzoladzola, pamene minofu ndi excised milomo.
Pamene ndiwofatsa chithandizo zotsatira zabwino chingapezeke ndi osakaniza corticosteroids, mankhwala ozunguza bongo antimalarial. "Prednisolone" ndi dera limodzi ndi "gentamycin". Ikani pyrogenic ndi zakupha chikumbumtima wothandizira. mankhwala NTHAWI ZONSE bakiteriya. Ngati wodwala tcheru staphylococcus, ndiye likukhudza "toxoid".
Wodwalayo ndi Melkersson-Rosenthal syndrome, Kuvomerezedwa multivitamins akuchipatala, kashiamu pantothenate, asidi nicotinic, vitamini A, unasankha "komplamin" Pakuti aziyenda bwino magazi zimakhala zofewa. ntchito Maphunzirowa - masiku 10. A bwino yoikika "Cavintonum", "Tanakan" ndi "stugeron" kumwedwa kwa miyezi 1 2. Odwala akatulutsidwa monga "Nerobolum". Izi ndi mankhwala kumathandiza ukalamba. Amaikidwa kukhala asamakhale ndi nkhawa ndiponso mankhwala.
chithandizo timitu
Kodi ndi njira zina zingagwiritsidwe ntchito kuthana ndi matenda Melkersson-Rosenthal? Chithandizo kungakhale apakhungu. Pa nthawi yomweyo anawagwiritsa ntchito ya heparin mafuta. Iwo kuphatikiza ndi Dimexidum, kusiya kwa mphindi 20. Ndondomeko ikuchitika 3 4 zina tsiku. Njira - masabata 3-4.
Pakuti mlomo wa mmunsi ntchito elektrofarez heparin. Ndondomeko anachita tsiku lililonse. Pamene ntchito fizlechenii mafunde Bernard, ndi helium-Neon laser ndi ultrasound.
Kugwiritsa corticosteroid ndi methyluracyl mafuta ntchito njira yotupa. nkhope chigoba umagwiritsidwa kwa mphindi 20, maulendo 2 3 tsiku. Komanso, ntchito anapangidwa kuchokera ndalama keratoplasty.
Ikani anatseka misewu (3-4 ml), ofunda awiri peresenti lidocaine wa, novocaine ndi trimecaine. Majekeseni anapangidwa tsiku lililonse kapena masiku awiri.
Zotsatira za matenda Melkersson-Rosenthal
Syndrome msanga amakhala aakulu. Izi kwambiri zimaonekera maonekedwe a munthu, amene akupotoza ndi ziwalo kutupa. Against maziko kawirikawiri ndi maganizo ndi mavuto a m'maganizo. Chifukwa kuchuluka kulephera kuyenda kwa milomo ndi munthu movutikira kutafuna ndi kumeza kulankhula kupotoza zimawonedwa. Ming'alu kuti kuonekera pamene kutupa ndipo angayambe tizilombo toyambitsa matenda kuchititsa matenda opatsirana. Imeneyi imagwiranso chinenero. Nthawi yokutidwa ndi ming'alu. Komanso, izi kumachititsa chifukwa choipa edematous mano mucosa Mwachitsanzo, pa kutafuna chakudya.
Anthu odwala matenda, Ndi bwino kudya chakudya chotafuna more: maphunziro oyamba, zosiyanasiyana dzinthu ndi mkaka. Izi mosavuta kutafuna chakudya ndipo kumachepetsa mosavuta kuvulala kwa mucosa m'kamwa. Zipatso ndi masamba ndi zothandiza, koma ayenera kudula mu magawo ang'ono ndi kuwonjezera kwa saladi. chunks Large chakudya chilichonse bwino pogaya mu ntchito mafoloko ndi mipeni chakudya.
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