Syndrome Budd-Chiari

Budd-Chiari syndrome kumachitika chifukwa ndi kufafaniza mwapang'onopang'ono (kutseka kapena kuchepetsa) ndi lumen wa mtsempha kukhetsa mu chiwindi. Chiari ankakhulupirira kuti chifukwa chachikulu - kutukusira yoyamba ya mitsempha kwa chiwindi. Koma patapita anazindikiritsidwa mu zina, pamene thrombosis ya mitsempha kwa chiwindi ndi otsika vena cava.

mabuku limafotokoza pafupifupi 200 milandu kuwononga endoflebita mu kwa chiwindi mitsempha (matenda , Budd-Chiari syndrome).

Ndi chitukuko cha thrombophlebitis arantsieva ritsa, amene imaphwera mwachindunji mu kumanzere kwa chiwindi mtsempha, umbilical mtsempha, ndi matenda izi zikhoza kukhala ana aang'ono. Chipolopolo mkati mwa mitsempha kwa chiwindi kapena otsika vena Vienna (pafupi confluence a chiwindi) ikukula, nthawi zina limodzi ndi magazi kuundana. Zonsezi zimayambitsa kutsekera kapena kuchepetsa wa lumen wa mtsempha, amene nawonso, chimachititsa chitukuko cha stagnation ndi psinjika maselo chiwindi.

Budd-Chiari syndrome akufotokozera mwa pathologies ena: neoplasms zilonda a chiwindi, kapamba, impso, etc., matenda mtima zowombetsa mkota chikhalidwe. Matenda enaake zingatithandizenso ndi kuchepetsa wa mitsempha kwa chiwindi. Chiari syndrome zikhoza pa kutanthauzira ena Gunma echinococcosis, actinomycosis, abscesses ndi zina zotero.

Kukomoka, Budd-Chiari syndrome kuwonetsera zizindikiro za matenda waukulu, zinapangitsa kuwonetsera zina komanso amadalira nthawi ya occlusion ya mitsempha. Pamene chionekera lakuthwa ndi zikamera mwapang'onopang'ono matendawa.

Pachimake kwa chiwindi mtsempha occlusion amachititsa maonekedwe mwadzidzidzi kusanza, kupweteka kwa nusu pomwe chapamwamba kapena epigastrium chifukwa kutupa kwa chiwindi, komanso hyperextension Glisson kapisozi, akufotokozera ascites, pali yellowness yaing'ono.

Portal oopsa akufotokozera pa nthawi yomweyo chifukwa cha kuwonjezeka mofulumira kuthamanga mu sinusoids kwa chiwindi ndi mitsempha.

Ascites ndi matenda si n'ngochiritsika ndi okodzetsa, madzimadzi chimamangirira kwambiri mwamsanga pambuyo paracentesis, nthawi zina chikondwerero kulowa magazi ake, angathe hydrothorax. Ngati akulowa thrombosis kuti akufotokozera mu otsika vena cava, ndiye pali kutupa mu malekezero m'munsi, "Medusa mutu", ndi kuthamanga kuwunika ntchito kwa izo, magazi ukupita mmwamba.

Ndi kukula kwa chiwindi mtsempha occlusion okwana akulowa thrombosis mesenteric, pali ululu ndi kutsekula m'mimba, zosokonezeka ubongo kuoneka chifukwa choipa chiwindi maselo amene amatha kufa pasanathe masiku ambiri.

Nthawi zina matenda Budd - Chiari, ndi kutsekedwa tsankho wa lumen wa mtsempha kumachitika monga matenda aakulu kwa nthawi yaitali. Ndi chikhalidwe ngati cha otaya nthawi limapezeka ina kufalitsidwa: dilate zachiphamaso khungu mtsempha, matenda oopsa zipata kutuluka, ndipo amayamba ndi esophageal mitsempha varicose.

Pakuti matenda n'kofunika pamaso pa yafupika kuthamanga mu mitsempha occlusal chiwindi ndi munthawi yomweyo kuenjezera kuthamanga zipata, umene wapezeka mwa njira hepato- ndi splenomanometrii. Ntchito retrograde rentgenogepatografiya imene wothandizila Mosiyana tikuuzidwa mu mtsempha kwa chiwindi. diagnostics ultrasound zachokera zizindikiro mwachindunji - kulingalira ndi magazi aumirira ku mitsempha.

Popanda mtundu doplerrovskogo maphunziro amati syndrome Budd-Chiari mu:

• Kupezeka kwa kusintha akakufunsani mu chiwindi, khalidwe la aakulu mafuta m'chiwindi kapena fibrosis a minofu chiwindi,

• The chithunzi palibe mitsempha kwa chiwindi, misa Mwachitsanzo, chifukwa kukhalapo mu lumen awo sakusiyana HIV mu lumen wa,

• ndi kuchepetsa wa otsika vena cava,

• zizindikiro za matenda oopsa zipata, ngati nthendayo yaitali.