Syndrome West

Kwa nthawi yoyamba zachilendo infantile spasms yatchedwa ndi West mu 1841st lapansi. Ndiye funso mwana wake. Makamaka anatsindika mosalekeza patsogolo zizindikiro psychomotor mu. Matendawa imatengedwa osachiritsika.

syndrome West m'gulu zizindikiro wa ku khalidwe - mobwerezabwereza mndandanda wa spasms, psychomotor retardation, lofotokoza kusintha (paroxysmal) pa akugwirira. Yambani pang'onopang'ono, zizindikiro woyamba mwina zimachitika ngakhale ana athanzi kale, ngakhale amaugwiritsa ndi maziko a aakulu psychomotor yomweyo. More zofala ana Miyezi inayi mpaka isanu ndi umodzi, koma n'zotheka matenda kenako (mpaka zaka zinayi). Anyamata poyera kuti matenda ambiri.

Infantile spasms zambiri symmetrical, amgwirizano, lalifupi, ndi chidule mwadzidzidzi magulu minofu. kuukira khalidwe zimadalira magulu nawo mbali (flexor, extensor). Omangana akhoza kufalitsa mwina akatumba onse kapena munthu (minofu khosi, minofu ya pamimba). Ambiri amene spasms wosanganiza, kenako kuwanda - flexor, ngakhale n'kukhala - ndi extensor. Komanso, pali kuphipha limadalira makamaka udindo wa thupi.

syndrome West zambiri kuzindikira spasms ndendende flexor. Ngati mukuchita m'mimba minofu flexors, thupi zambiri apangidwe mu theka. Pamene mtsikana chapamwamba malekezero, manja zimagwiridwa zithunzi-kubweretsa (zikuoneka kuti Yesuyo akuyamba akukumbatirana). Ndi okhudzidwa minofu flexor wa khosi kupsa ngati nodding. Ngati minofu mtsikana wa lamba phewa, mwana monga shrugs. Spasms lingachepetse kayendedwe nistagmoidnymi kapena kunjenjemera wa mwana wa m'diso la. N'zotheka ndi kupuma kulephera. Uyu ndiye woyamba zizindikiro za khunyu.

Mtundu wa spasms wa etiology sadalira, monga salola kulosera za chitukuko cha matenda. Komabe, ntchito ndi kukhalapo chosokonekera (asymmetry limasonyeza yokhudza kotekisi chotupa). spasms asymmetric atsimikiziridwa Mwachitsanzo, maso lateral-kutsogolera kapena mutu.

Spasms zambiri zimachitika pa Atauka kapena kugwa mwana tulo. Pasanathe mphindi imeneyi therebetween. Mphamvu ukuwonjezeka, ndiye amachepetsa. Osiyana pafupipafupi - kuchokera spasms umodzi mazana patsiku. Iwo akhoza chifukwa cha phokoso lalikulu kapena chogwirika.

Nditabwerera nthawi omangana yafupika reactivity. Kids amene kale kupita, kwadzidzidzi kugwa (dontho kuukira).

syndrome West akuti ndi mtundu ambiri encephalopathy khunyu, zikubweretsa kuwonongeka chidziwitso. Pa kupewa palibe deta.

syndrome West kumachitika chifukwa zifukwa zosiyanasiyana. Asphyxia - ambiri. Komanso, izo zikanakhoza kukhala chosayenerera kobadwa nako ubongo, intracranial kukha mwazi, ndi zina zotero. Nthawi zina chifukwa cha matenda sangakhoze zotsimikizika.

Ngati mwana wanu West syndrome, chithandizo akuyamba yomweyo. Mukhoza kusankha mankhwala mankhwala, ndipo n'zotheka kuti alowererepo chofunika, ndi madokotala amene kuchotsa pakati pathological, ili kwinakwake mu ubongo. Kalanga, mwai kupeza malo sikuti kuchitika, ndipo nthawi zina ngakhale pamene wapezeka, n'zosatheka kuchotsa.

Ngati mankhwala chofunika pochitika Inde amalandira yapadera, payekha anasankha mankhwala antiepileptic. Kutha kwa khunyu idzachitira umboni bwino mankhwala Komabe, mankhwala ayenera anawonjezera kuti khumi (ndi osachepera) miyezi. zinachitikira chipatala lingaliro chikhululukiro khola la matenda 60% ya ana, kuukira otsalira, mwatsoka, zimasinthidwa.

madokotala Israeli kunena, matenda ndi cryptogenic mawonekedwe madokotala ananena zawo bwino kwambiri. Akayakaya kuukira kuwombera, mwanayo "tikulirepo kuposa" syndrome, kakulidwe kuchedwa kusintha masewera ophunzitsa. Pamene symptomatic mawonekedwe a madokotala ananena zawo poipa. Ngati ife kutsindikiza kumpolozera oukira ndi kuthetsa gwero la isanayambike matenda (malformation, zotupa, cysts), ndi kukonzanso kugonjetsa zovuta kukhalabe mkulu.