ThanziMatenda ndi zokwaniritsa

Pancytopenia - chikhalidwe pathological amene amachepetsa mu magazi kufalitsidwa kwa zinthu zonse zikuchokera. Zoyambitsa, zizindikiro, chithandizo

Aliyense chitukuko cha matenda m'thupi zimayambitsa kusintha mu ntchito kwa magazi zotumphukira. Komabe, pali zingapo pathologies umene kusintha kumeneku ndi chachikulu matenda Mbali. Pancytopenia - ndi imodzi mwa njira pathological a dongosolo hematopoietic, amene anafotokozedwa monga matenda wodziimira, kapena mwina kumasonyeza ena concomitant nosological.

Zikhulupiriro General

Matendawa si wamba, anthu ambiri sadziwa chodabwitsa amenewa. Pancytopenia - khalidwe la kuperewera kwa maselo a magazi, chitukuko cha zomwe zimachitika chifukwa cha kuvutika mu kapangidwe ka maselo kalambulabwalo magazi pa siteji ya hematopoiesis. Yafupika kuchuluka kwa maselo ofiira, maselo oyera ndi maselo othandiza magazi kuundana chifukwa chakuti maselo tsinde sangathe mokwanira bwinobwino.

Matendawa akufotokozera m'njira ziwiri:

  • idiopathic, chifukwa cha zinthu mkati;
  • yachiwiri, chimene chayambitsa ndi zinthu kunja.

A chikhalidwe pathological m'ma 50% milandu akufotokozera autoimmune mtundu. Ndiko kuti, thupi kumenyana yekha ndi maselo magazi anu, mistaking iwo wothandizila yachilendo. mawonekedwe Idiopathic zingachitike ndi kuphatikana atsopano chinthu kunja kuti Iyamba zotsatira chowawa.

Pancytopenia - matenda amene akhoza tinatengera, kukhala pa nthawi imene mwana m'mimba. Mwana wabadwa kale ndi matenda a ziwalo magazi kupanga. Zimakhala kobadwa nako ndi mafupa hypoplasia, kotero kuti dongosolo sangathe kulimbana ndi ntchito zawo.

The etiology matenda chiopsezo zinthu

Mwa mavuto akuluakulu amene amayambitsa chitukuko cha matenda masinthidwe chibadwa, ntchito yaitali mankhwala, nyukiliya kapena zotsatira poizoni. mawonekedwe Idiopathic amakhala ndi chakuti chifukwa sangathe udzakhazikitsidwa Komabe, panali milandu matenda pambuyo wobereka.

Kukhazikitsa zifukwa n'kofunika kuti zinthu ziwayendere bwino. Kuthetsa kunja zoipa chikoka mu matenda - 50% bwino.

Kuwonjezera zifukwa zazikulu pali zifukwa zingapo zimene zimathandiza kuti chitukuko cha kudwala ndi:

  • Ntchito ndi benzene kapena Arsenic;
  • Fanconi magazi m'thupi;
  • chikhalidwe tizilombo matenda a AIDS;
  • Morning;
  • mankhwala ndi immunosuppressants;
  • matenda autoimmune monga zokhudza zonse lupus erythematosus;
  • radiotherapy.

Fanconi magazi m'thupi - chimodzi mwa zinthu etiological wa pancytopenia. Mpatuko pa maziko a anomalies kobadwa nako amati ndi autosomal recessive matenda. Magazi m'thupi amakhala ndi kukhalapo kwa zopindika mbali ya mapuloteni udindo DNA kukonza ndi khromozomu friability.

The matenda chithunzi cha matenda

chikhalidwe Pathological kumaonekera mwa mawonekedwe a syndromes atatu. Aliyense wa zinthu izi khalidwe kuchepetsa chiwerengero cha mtundu wina wa maselo a mwazi. Leukopenia kukuonetsedwa chithunzi cha sepsis pachimake ndi zikamera njira chilonda-necrotic mwa khungu nembanemba mucous.

Erythropenia ndi Amowabu kuchepetsa hemoglobin imautsa chitukuko cha zizindikiro za kuchepa kwa magazi m'thupi. boma amakhala ndi:

  • paleness wa khungu integument;
  • ntchentche pamaso ake ;
  • chizungulire;
  • tinnitus;
  • kufooka ndi kutopa;
  • kufooka.

Odwala amadandaula kufupika kwa mpweya ndi mtima palpitations. Auscultation kudziwa malankhulidwe opanda mtima, systolic kudandaula pa nkhope yonse ya ziyerekezo mtima, phokoso la pamwamba pa mtsempha jugular. Akuchuluka wa alili amachititsa kusintha electrocardiogram, amene amasonyeza chitukuko cha matenda a mtima.

Thrombocytopenia akuwonetseredwa ndi pafupipafupi magazi (epistaxis, m'mimba, uterine), magazi m'kamwa, maonekedwe a petechiae ndiponso kukha magazi pakhungu. Zizindikiro pachimake cha matenda imapachikidwa kwa mwezi umodzi ndipo nthawi zambiri amatha kufa. Matenda pancytopenia analola yabwino kwambiri ndipo ali ndi zizindikiro zochepa kutchulidwa

matenda imatengedwa kukhala zovuta. Pancytopenia, zomwe mavuto ndi ambiri kwa anthu okalamba, limodzi ndi maonekedwe a matenda a magazi.

miyeso matenda

Mlandu amafuna kungapezeke kuti kuyendera katswiri, mbiri deta ndi moyo wa wodwalayo. Komanso yoikidwiratu malamulowa. Pankhani ya zolozerazi angaonetse pa zomwe pancytopenia ndi kuchititsa miyeso zina matenda:

  • leukocytes <2 × 109 / l;
  • othandiza magazi kuundana <150 × 109 / L;
  • erythrocytes <3,5 × 109 / l.

Anatumizidwa kuphunzira puncture mafupa, amene amasonyeza kupezeka kwa maselo nthenda ndi myelokaryocytes. Tsimikizani ndi kukhalapo kwa kuvutika, kuphatikizapo mafupa hypoplasia. Imachitikanso zitsanzo hemolytic.

pancytopenia chithandizo

masitepe achire zimadalira nkhani ovutika alili ndi chinthu etiological kuti zimayambitsa matendawo ayi. Zotsatirazi mankhwala njira angagwiritsidwe ntchito:

  • Magazi, pofuna kukwaniritsa bwino zinthu mawonekedwe.
  • Kupatsidwa zina za mafupa kapena tsinde maselo. Nthawi zambiri odwala achinyamata ndi zapakatikati.
  • Pankhani ya pancytopenia autoimmune kutumikiridwa ntchito immunosuppressant "Cytoxan", "Methylprednisolone," "Neoral", "Sandimun".
  • Zikutanthauza zolimbikitsa ndi mafupa ntchito - "Neupogen", "Neulasta", "Procrit", "Leukin".

zomera mankhwala

Zovuta matenda mankhwala zikuphatikizapo kugwiritsa ntchito mankhwala azitsamba. Mlingo wa maselo ofiira ndi hemoglobin angaukitsidwe kukhala mothandizidwa ndi zipatso. teas zokhalamo anapangidwa pamaziko a phulusa, wakuda currants, ananyamuka m'chiuno, strawberries, zipatso, apurikoti. Kusita wolemera turnips, gooseberries, yamatcheri ndi mphesa, kudya zomwe sitikanati kukwaniritsa bwino maselo a magazi, komanso kulimbikitsa chitetezo cha m'thupi.

zingapo njira wowerengeka zochepetsera pancytopenia limapangidwa uchi. Iwo pamodzi ndi mankhwala zotsatirazi:

  • ndi vinyo wofiira ndi aloe;
  • adyo;
  • Mapila;
  • mandimu, apricots zouma zoumba prunes ndi walnuts.

Kofunika kwambiri infusions ndi decoctions zitsamba mankhwala nettle nettle, birch, udzu tchire, clover, dandelion maluwa clover, buckwheat.

Pomaliza

Pancytopenia - matenda aakulu, limene limasonyeza kuti nthenda yomwe imapha. Zotsatira zimadalira popereka zizindikiro matenda, maonekedwe ndi magawo chitukuko imene chithandizo anayamba. matenda amenewa ndi kosavuta kupewa kuposa kuchiza.

The mankhwala Kupenda pachaka anthu zimalimbikitsa chizindikiritso cha chikhalidwe pathological mu magawo oyambirira. Makamaka zimenezi zikugwira ntchito njira zasayansi bwino.

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