ThanziMatenda ndi zokwaniritsa

The anomaly wa Arnold Chiari

Anomaly Arnold Chiari limodzi dystopia (kuphwanya malo) nyumba mu zapambuyo cranial fossa kuchepetsa iwo kudzera lalikulu inabala khosi kunja chigaza mu ngalande msana. kosangalatsa A cerebellar tonsils kapena mbali kwa kumtunda kwa ngalande vertebral.

Pali mitundu zinayi za matenda. Anomaly Arnold Chiari Mtundu 1 Titha kuchepetsa tonsils cerebellar, osati limodzi ndi zina chitukuko anomalies ubongo. Mtundu m'zimene anthu patatha zaka makumi atatu. Mtundu wachiwiri wa kuphwanya malo a nyumba za mu zapambuyo fossa ndi tonsils cerebellar. Nthawi zambiri mtundu amawapeza ana. A mtundu wachitatu malo anomaly monga kuyan'anila pafupifupi nyumba zonse fossa zadnecherepnoy. Chiwonetsero cha mtundu uwu si yogwirizana ndi moyo. Yachinayi ya anomaly ndi analandira ankaona ngati kusuntha kwa underdevelopment wa cerebellum lapansi. Modern neurosurgery anafotokoza kuti syndrome zokoma-Walker.

Mu cerebellum indentation mu gawo kumtunda kwa ngalande msana ndi kusokonezeka kwa yachibadwa outflow mowa amateteza ubongo ndi msana. Kuvutika kupezeka CSF zingachititse blockage wa chizindikiro kuchokera ubongo ziwalo kapena kudzikundikira madzimadzi cerebrospinal. Kuthamanga kuti cerebellum ali pa chingwe msana angachotsedwe syringomyelia.

Malinga ndi akatswiri ambiri, Arnold Chiari anomaly imatengedwa kuti ndi matenda otengera kwa makolo. Komabe, tisaiwale kuti maphunziro umalimbana kufufuza chinthu ichi, ndi pa siteji koyamba.

odwala ambiri amene ali ndi vuto limeneli, si anati zizindikiro kapena zizindikiro. odwala amalandira palibe mankhwala. Kudziwika matenda amapezeka okha matenda a matenda ena.

Kukula kwa matenda nthawi zambiri limodzi ndi mutu, chikwiyire ndi kutsokomola, sneezing kapena mopambanitsa thupi, dzanzi ndi kumva kulasalasa mu manja, kuphwanya kutentha-tcheru ndipo zotsatira zake, kawirikawiri amayaka. Ndiponso, kwa matenda yodziwika ndi ululu mu khomo lachiberekero kapena khomo lachiberekero dera, kwa nthawi mumbali mapewa. Pali mavuto chingakuthandizeni (m'goli gait) ndi chifooke kugwirizana dzanja.

Chifukwa ambiri mwa zizindikiro za matenda amaganizira ndi matenda, m'pofunika kuti akudwala matenda wathunthu.

Matenda miyeso kuyamba ndi kuyamba kuona ndi kuyankhulana mtima. Ngati wodwala anadandaula za ululu m'mutu, koma chifukwa asayembekezere si bwino kuti munthu waluso, izo ndi nkhani Kujambula. Diagnostics amalola zokwanira molondola kudziwa pamaso pa matenda.

Nthawi zina, Arnold Chiari anomaly limakhala matenda mwapang'onopang'ono kuti kumabweretsa mavuto aakulu kwambiri. Zikuphatikizapo hydrocephalus (madzimadzi owonjezera mu ubongo). Choncho pali kufunika kwa chubu kusintha kwa ikukoka madzimadzi cerebrospinal kudera lina la thupi. Zovuta za matendawa monga ziwalo. Akufotokozera chifukwa cha psinjika msana. Syringomyelia anafotokoza komanso mavuto zotheka. Iwo limodzi ndi mapangidwe cysts mu msana kapena M'mimbamo, wodzala ndi madzimadzi cerebrospinal ndi kupereka ntchito.

Odwala amene Arnold-Chiari chosayenerera chithandizo wapatsidwa malinga ndi kukula kwa chikhalidwe. Popeza zizindikiro zambiri zoikidwa ndi kuwunika zonse ndi chiphasochi. Pamene mawonetseredwe a zizindikiro za dokotala chachikulu mwina mankhwala othetsa ululu. Komabe, ambiri mwa mankhwalawa matenda chikachitika opaleshoni.

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